S.No. Ailment Name Metabolism Cycle Enzyme Action
1 Methacrylic aciduria / 3-Hydroxy-isobutyryl-CoA hydrolase (HIBCH) deficiency /Leigh-like disease carbohydrate Propanoate metabolism 3Hydroxy-Propanoate?3Hydroxy-propionyl-CoA3-Hydroxyisobutyryl-CoA hydrolase (3.1.2.4)(2q32.2) View
2 Methacrylic aciduria / 3-Hydroxy-isobutyryl-CoA hydrolase (HIBCH) deficiency /Leigh-like disease protein Valine , Leucine, and Isoleucine Degradation (S)-3-Hydroxyisobutyryl-CoA?..(S)-3-Hydroxyisobutyrate 3-Hydroxyisobutyryl-CoA hydrolase (EC:3.1.2.4) 2q32.2 View